Fig. 1

Fiber size comparison between control and CFZS patients. (A) Representative images of a single fiber from a control and from each of the CFZS patients (114 fibers from seven controls and 32 fibers from two CFZS patients) red is desmin and blue is dapi (B) Fiber CSA for controls and CFZS patients. (C) Relative frequency of Fiber CSA is presented as median ± interquartile range and significance was determined by Mann Whiney test, **** represents a p value of < 0.0001